Vaka 12

Özet

Subependimal dev hücreli astrositomlar, genellikle tuberoskleroz ile ilişkili, foramen Monro çevresinde yerleşen düşük dereceli tümörlerdir. BOS akımını tıkayarak hidrosefaliye yol açabilirler. MRG’de T1 izo/hipointens, T2 hiperintens olup belirgin kontrast tutulumu gösterirler. Cerrahi tedavi temel yaklaşımdır.

Referanslar

Mizuguchi M, Takashima S. Neuropathology of tuberous sclerosis. Brain and Development. 2001;23(7):508-515.doi:10.1016/s0387-7604(01)00304-7

de Ribaupierre S, Dorfmüller G, Bulteau C, et al. Subependymal giant-cell astrocytomas in pediatric tuberous sclerosis disease: when should we operate? Neurosurgery. 2007;60(1):83-89; discussion 89-90.doi:10.1227/01.Neu.0000249216.19591.5d

Mei G-H, Liu X-X, Zhou P, et al. Clinical and imaging features of subependymal giant cell astrocytoma: report of 20 cases. Chinese Neurosurgical Journal. 2017;3(1):14.doi:10.1186/s41016-017-0077-4

Kim JY, Jung TY, Lee KH, et al. Subependymal Giant Cell Astrocytoma Presenting with Tumoral Bleeding: A Case Report. Brain Tumor Research and Treatment. 2017;5(1):37-41.doi:10.14791/btrt.2017.5.1.37

Rott HD, Lemcke B, Zenker M, et al. Cyst-like cerebral lesions in tuberous sclerosis. American Journal of Medical Genetics. 2002;111(4):435-439.doi:10.1002/ajmg.10637

Matsumura H, Takimoto H, Shimada N, et al. Glioblastoma following radiotherapy in a patient with tuberous sclerosis. Neurologia medico-chirurgica (Tokyo). 1998;38(5):287-291.doi:10.2176/nmc.38.287

Krueger DA, Care MM, Agricola K, et al. Everolimus long-term safety and efficacy in subependymal giant cell astrocytoma. Neurology. 2013;80(6):574-580.doi:10.1212/WNL.0b013e3182815428

Sayfalar

67-70

Yayınlanan

24 Aralık 2025

Lisans

Lisans