Bilier Atrezi
Özet
Referanslar
Thomson J. On congenital obliteration of the bile ducts. Edinburgh Med J. 1891;37:523–31, 604–16, 724–735.
Ladd WE. Congenital atresia and stenosis of the bile ducts. JAMA. 1928;91:1082–1085.
Sterling JA. Experiences with Congenital Biliary Atresia. Springfield, IL: Charles C Thomas; 1960:3–68.
Fonkalsrud EW, Kitagawa S, Longmire WP. Hepatic drainage to the jejunum for congenital biliary atresia. Am J Surg. 1966;112:188 194.
Kasai M, Suzuki S. A new operation for non-correctable biliary atre sia: Hepatic portoenterostomy. Shujutu. 1959;13:733–739.
Ryckman F, Fisher R, Pedersen S, et al. Improved survival in biliary atresia patients in the present era of liver transplantation. J Pediatr Surg. 1993;28:382–385.
Kilgore A, Mack CL. Update on investigations pertaining to the pathogenesis of biliary atresia. Pediatr Surg Int. 2017;33:1233 1241.
Davenport M. Updates in Biliary Atresia: Aetiology, Diagnosis and Surgery. Children (Basel). 2025 Jan 16;12(1):95. doi: 10.3390/children12010095. PMID: 39857926; PMCID: PMC11764285.
Davenport M, Savage M, Mowat AP, et al. The biliary atresia splenic malformation syndrome. Surgery. 1993;113:662–668.
Jacquemin E, Cresteil D, Raynaud N, et al. CFC1 gene mutation and biliary atresia with polysplenia syndrome. J Pediatr Gastroenterol Nutr. 2002;34:326–327.
Wu LN, Zhu ZJ, Sun LY. Genetic Factors and Their Role in the Pathogenesis of Biliary Atresia. Front Pediatr. 2022 Jun 29;10:912154. doi: 10.3389/fped.2022.912154. PMID: 35844731; PMCID: PMC9277099.
Silveira TR, Salzano FM, Donaldson PT, et al. Association between HLA and extrahepatic biliary atresia. J Pediatr Gastroenterol Nutr. 1993;16:114–117.
Dillon P, Belchis D, Tracy T, et al. Increased expression of intercellular adhesion molecules in biliary atresia. Am J Pathol. 1994;145:263 267.
Kobayashi H, Horikoshi K, Li L, et al. Serum concentration of adhe sion molecules in postoperative biliary atresia patients: relationship to disease activity and cirrhosis. J Pediatr Surg. 2001;36:1297 1301.
Schreiber RA, Harpavat S, Hulscher JBF, Wildhaber BE. Biliary Atresia in 2021: Epidemiology, Screening and Public Policy. J Clin Med. 2022 Feb 14;11(4):999. doi: 10.3390/jcm11040999. PMID: 35207269; PMCID: PMC8876662.
Chung PHY, Zheng S, Tam PKH. Biliary atresia: East versus west. Semin Pediatr Surg. 2020 Aug;29(4):150950. doi: 10.1016/j.sempedsurg.2020.150950. Epub 2020 Jul 23. PMID: 32861448.
Xu Y, Yu J, Zhang R, Yin Y, Ye J, Tan L, Xia H. The perinatal infection of cytomegalovirus is an important etiology for biliary atresia in China. Clin Pediatr (Phila). 2012 Feb;51(2):109-13. doi: 10.1177/0009922811406264. Epub 2011 Dec 5. PMID: 22144720.
Lakshminarayanan B, Davenport M. Biliary atresia: A comprehensive review. J Autoimmun. 2016 Sep;73:1-9. doi: 10.1016/j.jaut.2016.06.005. Epub 2016 Jun 23. PMID: 27346637.
Ergün, O. biliary atresia. Turk. Assoc. Pediatr. Surg. 2017, 31, 46–55, https://doi.org/10.5222/jtaps.2017.1011.
Palmer RH, Ezhuthachan S, Newman C, et al. Mana gement of hyperbilirubinemia in newborns: measuring performance using a benchmarking model. Pediatrics 2004;114:902.
Lin JS, Chen SC, Lu CL, et al. Reduction of the ages at diagnosis and operation of biliary atresia in Taiwan: a 15-year population-based cohort study. World J Gastroenterol. 2015;21:13080–13086.
Abramson SJ, Berdon WE, Altman RP, et al. Biliary atresia and non cardiac polysplenia syndrome: ultrasound and surgical consider ation. Radiology. 1987;163:377–379.
Zhou L, Shan Q, Tian W, et al. Ultrasound for the diagnosis of biliary atresia: a meta-analysis. AJR Am J Roentgenol. 2016;206: W73–W82.
Masturina M, Prihaningtyas RA, Setyoboedi B, Arief S. Late Referral of Biliary Atresia and Poor Clinical Outcomes. Korean J Gastroenterol. 2025 Jul 25;85(3):382-388. doi: 10.4166/kjg.2025.005. PMID: 40709428.
Tian Y, Lian H, Ye M, Shao Y, Geng Y, Chen Z, Chen S, Xuli, Longli. Evaluating the role of Kasai portoenterostomy in biliary atresia older than 90 days. Pediatr Surg Int. 2025 Sep 4;41(1):285. doi: 10.1007/s00383-025-06184-7. PMID: 40908322.
Davenport M, Superina R. Primary Liver Transplant in Biliary Atresia: The Case for and Against. J Pediatr Surg. 2024 Aug;59(8):1418-1426. doi: 10.1016/j.jpedsurg.2024.03.005. Epub 2024 Mar 14. PMID: 38565475.
Priya Ramachandran, Mohamed Safwan, Sankaranara yanan Srinivas, et al. The extended Kasai portoenteros tomy for biliary atresia: A preliminary report. J Indian Assoc Pediatr Surg 2016;21(2):66-71.
Bezerra JA, Spino C, Magee JC, et al. Use of corticosteroids after hepa toportoenterostomy for bile drainage in infants with biliary atresia: the START randomized clinical trial. JAMA. 2014;311:1750 1759.
Tyraskis A, Davenport M. Steroids after the Kasai procedure for bili ary atresia: the effect of age at Kasai portoenterostomy. Pediatr Surg Int. 2016;32:193–200.
Davenport M, Parsons C, Tizzard S, Hadzic N. Steroids in biliary atresia: single surgeon, single centre, prospective study. J Hepatol. 2013;59:1054–1058.
Japanese Biliary Atresia S, Nio M, Muraji T. Multicenter randomized trial of postoperative corticosteroid therapy for biliary atresia. Pediatr Surg Int. 2013;29:1091–1095.
Yamataka A, Kobayashi H, Shimotakahara A, et al. Recommenda tions for preventing complications related to Roux-en-Y hepatico jejunostomy performed during excision of choledochal cyst in children. J Pediatr Surg. 2003;38:1830–1832.
Cho YJ, Kwon H, Kwon YJ, Ha S, Kim SC, Kim DY, Namgoong JM. Surgical treatment for intractable cholangitis with intrahepatic biliary cysts followed by Kasai operation in biliary atresia: a retrospective cohort study. Ann Surg Treat Res. 2024 Dec;107(6):363-368. doi: 10.4174/astr.2024.107.6.363. Epub 2024 Dec 2. PMID: 39669384; PMCID: PMC11634395.
Lykavieris P, Chardot C, Sokhn M, et al. Outcome in adulthood of biliary atresia: a study of 63 patients who survived for over 20 years with their native liver. Hepatology. 2005;41:366–371.
Alkhasov A, Komina E, Ratnikov S, Saveleva M, Romanova E, Gusev A, Lochmatov M, Yatsyk S, Dyakonova E. Surgical Treatment of Portal Hypertension in Children. J Laparoendosc Adv Surg Tech A. 2023 Dec;33(12):1231-1235. doi: 10.1089/lap.2022.0404. Epub 2023 Oct 16. PMID: 37844079.
Sokol RJ, Shepherd RW, Superina R,et al. Screening and Outcomes in Biliary Atresia: Summary of a Nati onal Institutes of Health Workshop. Hepatology 2007, 46;2:566-581. https://doi.org/10.1002/hep.21790
Farooqui ZA, Hartman SJ, Stetson AE, Schepers EJ, Speck KE, Gadepalli SK, Van Arendonk KJ, Georgeades C, Lal DR, Deans KJ, Minneci PC, Apfeld JC, Saito JM, Mak GZ, Slidell MB, Lemoine C, Superina R, Wright TN, Downard CD, Devara LP, Hirschl RB, Landman MP, Leys CM, Markel TA, Rymeski B, Mullapudi B, Tiao GM; Midwest Pediatric Surgery Consortium. Real-world Multi-institutional Data From the Midwest Pediatric Surgery Consortium (MWPSC) to Assess the Effect of Delayed Kasai Procedure on Biliary Drainage in Patients With Biliary Atresia. J Pediatr Surg. 2025 May;60(5):162250. doi: 10.1016/j.jpedsurg.2025.162250. Epub 2025 Feb 18. PMID: 40023993.
Davenport M. Updates in Biliary Atresia: Aetiology, Diagnosis and Surgery. Children (Basel). 2025 Jan 16;12(1):95. doi: 10.3390/children12010095. PMID: 39857926; PMCID: PMC11764285.
Davenport M, Makin E, Ong EG, Sharif K, Dawrant M, Alizai N. The Outcome of a Centralization Program in Biliary Atresia: Twenty Years and Beyond. Ann Surg. 2025 Apr 1;281(4):608-614. doi: 10.1097/SLA.0000000000006273. Epub 2024 Mar 20. PMID: 38506040.
Nio M. Japanese biliary atresia registry. Pediatr Surg Int. 2017;33: 1319–1325.
Referanslar
Thomson J. On congenital obliteration of the bile ducts. Edinburgh Med J. 1891;37:523–31, 604–16, 724–735.
Ladd WE. Congenital atresia and stenosis of the bile ducts. JAMA. 1928;91:1082–1085.
Sterling JA. Experiences with Congenital Biliary Atresia. Springfield, IL: Charles C Thomas; 1960:3–68.
Fonkalsrud EW, Kitagawa S, Longmire WP. Hepatic drainage to the jejunum for congenital biliary atresia. Am J Surg. 1966;112:188 194.
Kasai M, Suzuki S. A new operation for non-correctable biliary atre sia: Hepatic portoenterostomy. Shujutu. 1959;13:733–739.
Ryckman F, Fisher R, Pedersen S, et al. Improved survival in biliary atresia patients in the present era of liver transplantation. J Pediatr Surg. 1993;28:382–385.
Kilgore A, Mack CL. Update on investigations pertaining to the pathogenesis of biliary atresia. Pediatr Surg Int. 2017;33:1233 1241.
Davenport M. Updates in Biliary Atresia: Aetiology, Diagnosis and Surgery. Children (Basel). 2025 Jan 16;12(1):95. doi: 10.3390/children12010095. PMID: 39857926; PMCID: PMC11764285.
Davenport M, Savage M, Mowat AP, et al. The biliary atresia splenic malformation syndrome. Surgery. 1993;113:662–668.
Jacquemin E, Cresteil D, Raynaud N, et al. CFC1 gene mutation and biliary atresia with polysplenia syndrome. J Pediatr Gastroenterol Nutr. 2002;34:326–327.
Wu LN, Zhu ZJ, Sun LY. Genetic Factors and Their Role in the Pathogenesis of Biliary Atresia. Front Pediatr. 2022 Jun 29;10:912154. doi: 10.3389/fped.2022.912154. PMID: 35844731; PMCID: PMC9277099.
Silveira TR, Salzano FM, Donaldson PT, et al. Association between HLA and extrahepatic biliary atresia. J Pediatr Gastroenterol Nutr. 1993;16:114–117.
Dillon P, Belchis D, Tracy T, et al. Increased expression of intercellular adhesion molecules in biliary atresia. Am J Pathol. 1994;145:263 267.
Kobayashi H, Horikoshi K, Li L, et al. Serum concentration of adhe sion molecules in postoperative biliary atresia patients: relationship to disease activity and cirrhosis. J Pediatr Surg. 2001;36:1297 1301.
Schreiber RA, Harpavat S, Hulscher JBF, Wildhaber BE. Biliary Atresia in 2021: Epidemiology, Screening and Public Policy. J Clin Med. 2022 Feb 14;11(4):999. doi: 10.3390/jcm11040999. PMID: 35207269; PMCID: PMC8876662.
Chung PHY, Zheng S, Tam PKH. Biliary atresia: East versus west. Semin Pediatr Surg. 2020 Aug;29(4):150950. doi: 10.1016/j.sempedsurg.2020.150950. Epub 2020 Jul 23. PMID: 32861448.
Xu Y, Yu J, Zhang R, Yin Y, Ye J, Tan L, Xia H. The perinatal infection of cytomegalovirus is an important etiology for biliary atresia in China. Clin Pediatr (Phila). 2012 Feb;51(2):109-13. doi: 10.1177/0009922811406264. Epub 2011 Dec 5. PMID: 22144720.
Lakshminarayanan B, Davenport M. Biliary atresia: A comprehensive review. J Autoimmun. 2016 Sep;73:1-9. doi: 10.1016/j.jaut.2016.06.005. Epub 2016 Jun 23. PMID: 27346637.
Ergün, O. biliary atresia. Turk. Assoc. Pediatr. Surg. 2017, 31, 46–55, https://doi.org/10.5222/jtaps.2017.1011.
Palmer RH, Ezhuthachan S, Newman C, et al. Mana gement of hyperbilirubinemia in newborns: measuring performance using a benchmarking model. Pediatrics 2004;114:902.
Lin JS, Chen SC, Lu CL, et al. Reduction of the ages at diagnosis and operation of biliary atresia in Taiwan: a 15-year population-based cohort study. World J Gastroenterol. 2015;21:13080–13086.
Abramson SJ, Berdon WE, Altman RP, et al. Biliary atresia and non cardiac polysplenia syndrome: ultrasound and surgical consider ation. Radiology. 1987;163:377–379.
Zhou L, Shan Q, Tian W, et al. Ultrasound for the diagnosis of biliary atresia: a meta-analysis. AJR Am J Roentgenol. 2016;206: W73–W82.
Masturina M, Prihaningtyas RA, Setyoboedi B, Arief S. Late Referral of Biliary Atresia and Poor Clinical Outcomes. Korean J Gastroenterol. 2025 Jul 25;85(3):382-388. doi: 10.4166/kjg.2025.005. PMID: 40709428.
Tian Y, Lian H, Ye M, Shao Y, Geng Y, Chen Z, Chen S, Xuli, Longli. Evaluating the role of Kasai portoenterostomy in biliary atresia older than 90 days. Pediatr Surg Int. 2025 Sep 4;41(1):285. doi: 10.1007/s00383-025-06184-7. PMID: 40908322.
Davenport M, Superina R. Primary Liver Transplant in Biliary Atresia: The Case for and Against. J Pediatr Surg. 2024 Aug;59(8):1418-1426. doi: 10.1016/j.jpedsurg.2024.03.005. Epub 2024 Mar 14. PMID: 38565475.
Priya Ramachandran, Mohamed Safwan, Sankaranara yanan Srinivas, et al. The extended Kasai portoenteros tomy for biliary atresia: A preliminary report. J Indian Assoc Pediatr Surg 2016;21(2):66-71.
Bezerra JA, Spino C, Magee JC, et al. Use of corticosteroids after hepa toportoenterostomy for bile drainage in infants with biliary atresia: the START randomized clinical trial. JAMA. 2014;311:1750 1759.
Tyraskis A, Davenport M. Steroids after the Kasai procedure for bili ary atresia: the effect of age at Kasai portoenterostomy. Pediatr Surg Int. 2016;32:193–200.
Davenport M, Parsons C, Tizzard S, Hadzic N. Steroids in biliary atresia: single surgeon, single centre, prospective study. J Hepatol. 2013;59:1054–1058.
Japanese Biliary Atresia S, Nio M, Muraji T. Multicenter randomized trial of postoperative corticosteroid therapy for biliary atresia. Pediatr Surg Int. 2013;29:1091–1095.
Yamataka A, Kobayashi H, Shimotakahara A, et al. Recommenda tions for preventing complications related to Roux-en-Y hepatico jejunostomy performed during excision of choledochal cyst in children. J Pediatr Surg. 2003;38:1830–1832.
Cho YJ, Kwon H, Kwon YJ, Ha S, Kim SC, Kim DY, Namgoong JM. Surgical treatment for intractable cholangitis with intrahepatic biliary cysts followed by Kasai operation in biliary atresia: a retrospective cohort study. Ann Surg Treat Res. 2024 Dec;107(6):363-368. doi: 10.4174/astr.2024.107.6.363. Epub 2024 Dec 2. PMID: 39669384; PMCID: PMC11634395.
Lykavieris P, Chardot C, Sokhn M, et al. Outcome in adulthood of biliary atresia: a study of 63 patients who survived for over 20 years with their native liver. Hepatology. 2005;41:366–371.
Alkhasov A, Komina E, Ratnikov S, Saveleva M, Romanova E, Gusev A, Lochmatov M, Yatsyk S, Dyakonova E. Surgical Treatment of Portal Hypertension in Children. J Laparoendosc Adv Surg Tech A. 2023 Dec;33(12):1231-1235. doi: 10.1089/lap.2022.0404. Epub 2023 Oct 16. PMID: 37844079.
Sokol RJ, Shepherd RW, Superina R,et al. Screening and Outcomes in Biliary Atresia: Summary of a Nati onal Institutes of Health Workshop. Hepatology 2007, 46;2:566-581. https://doi.org/10.1002/hep.21790
Farooqui ZA, Hartman SJ, Stetson AE, Schepers EJ, Speck KE, Gadepalli SK, Van Arendonk KJ, Georgeades C, Lal DR, Deans KJ, Minneci PC, Apfeld JC, Saito JM, Mak GZ, Slidell MB, Lemoine C, Superina R, Wright TN, Downard CD, Devara LP, Hirschl RB, Landman MP, Leys CM, Markel TA, Rymeski B, Mullapudi B, Tiao GM; Midwest Pediatric Surgery Consortium. Real-world Multi-institutional Data From the Midwest Pediatric Surgery Consortium (MWPSC) to Assess the Effect of Delayed Kasai Procedure on Biliary Drainage in Patients With Biliary Atresia. J Pediatr Surg. 2025 May;60(5):162250. doi: 10.1016/j.jpedsurg.2025.162250. Epub 2025 Feb 18. PMID: 40023993.
Davenport M. Updates in Biliary Atresia: Aetiology, Diagnosis and Surgery. Children (Basel). 2025 Jan 16;12(1):95. doi: 10.3390/children12010095. PMID: 39857926; PMCID: PMC11764285.
Davenport M, Makin E, Ong EG, Sharif K, Dawrant M, Alizai N. The Outcome of a Centralization Program in Biliary Atresia: Twenty Years and Beyond. Ann Surg. 2025 Apr 1;281(4):608-614. doi: 10.1097/SLA.0000000000006273. Epub 2024 Mar 20. PMID: 38506040.
Nio M. Japanese biliary atresia registry. Pediatr Surg Int. 2017;33: 1319–1325.