Parotidektomi Yapılan Charcot-Marie-Tooth Hastasında Anestezi Yönetimi

Çağdaş Baytar; Dinçer Fırat Şeker

doi:10.37609/akya.3402

Yazarlar

Çağdaş Baytar

https://orcid.org/0000-0001-7872-9676

Dinçer Fırat Şeker

https://orcid.org/0000-0003-4271-2631

DOI: https://doi.org/10.37609/akya.3402.c11300

Özet

Charcot-Marie-Tooth hastalığı sensörinöral bir periferik polinöropati olup periferik sinir sisteminin en yaygın kalıtsal bozukluğudur. İlerleyici kas güçsüzlüğü tipik olarak ergenlikte veya erken yetişkinlikte fark edilir hale gelir. Hem duyusal hem de motor sinirleri etkiler. Etkilenen sinirler yavaşça dejenere olur ve uzaktaki hedefleriyle iletişim kurma yeteneğini kaybeder, bu da kollarda, bacaklarda, ellerde veya ayaklarda kas güçsüzlüğü ve atrofiye neden olur. Bu olgu sunumunda kulak burun ve boğaz hastalıkları (KBB) tarafından parotidektomi yapılan 57 yaşındaki Charcot-Marie-Tooth tanılı erkek hastanın anestezi yönetimi tartışılmıştır.

Charcot-Marie-Tooth disease is a sensorineural peripheral polyneuropathy and the most common inherited disorder of the peripheral nervous system. Progressive muscle weakness typically becomes noticeable in adolescence or early adulthood. It affects both sensory and motor nerves. Affected nerves slowly degenerate and lose the ability to communicate with their distant targets, resulting in muscle weakness and atrophy in the arms, legs, hands or feet. In this case report, we discuss the anesthetic management of a 57-year-old male patient with Charcot-Marie-Tooth who underwent parotidectomy by Otorhinolaryngology.

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