Nöroimmünolojık Hastalıklarda Tanım ve Terminoloji
Özet
Nöroimmünolojik hastalıklar çocukluk döneminde çesitli semptom ve bulgularla karşımıza çıkan temelini immün ve inflamatuar süreçlerin oluşturduğu heterojen bir grup hastalıktır. Çoğu akut ve subakut başlangıçlı olmasına rağmen kronik süreçler ile de karşımıza cıkabilmektedir. Bu hastalıkların tanınması tedaviye yaklaşım açısından önemlidir. Genellikle kortikosteroid, intavenöz immunoglobulin, plazmaferez immunoterapilere iyi yanıt verirler. Bu bölümde çocuklarda sık görülen nöroimmunolojik hastalıklardan SSS ve periferik demiyelinizan hastalıkların, otoimmun ensefalitlerin, immün aracılı sinir-kas kavşak hastalıklarının, otoimmun epilepsilerin, paraneoplastik sendromların, otoimmun astrositopatilerin, otoimmun bazal ganglia hastalıklarının, immün ataksilerin tanımları verilecektir.
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